Double outlet right ventricle: aetiologies and associations

Double outlet right ventricle: aetiologies and associations.

BACKGROUND Double outlet right ventricle (DORV), a clinically significant congenital heart defect, occurs in 1-3% of individuals with congenital heart defects. In contrast to other major congenital heart defects, there are no systematic or comprehensive data regarding associations, aetiologies, and pathogenesis of DORV. We analysed reported cases in the medical literature to address these issue...

Double outlet right ventricle.

double-outlet right ventricle

In a previous study the possibility that tetralogy of Fallot and transposition of the great arteries may arise as a result of embryonic arrests in the normal rotation of the junction of the outflow tract and the great arteries was investigated. The results suggested that the development of other transposition complexes such as double-outlet right ventricle might also be related to arrests in th...

Double-outlet right ventricle with long survival.

The entity of double outlet right ventricle is being increasingly recognized in recent years (Neufeld, DuShane, and Edwards, 1961a; Neufeld et al., 1961b, 1962; Morgan et al., 1962; Mehrizi, 1965; Venables and Campbell, 1966). The oldest patient in the series reported by Mehrizi (1965) was 22 years and in the 10 patients of Venables and Campbell (1966) the oldest was 9 years. We report a patien...

Double Outlet Right Ventricle with Pulmonic Stenosis.

The results of complete repair of double-outlet right ventricle with pulmonic stenosis in 22 Mayo Clinic patients were analyzed. The overall mortality rate was 32%. Since 1960, the mortality rate has been reduced to 16%. Anomalies of the distribution of the right coronary artery, a second ventricular septal defect of the atrioventricular canal type, and significant residual pulmonic stenosis we...